Herlyn-Werner-Wunderlich syndrome: a rare cause of acute urinary retention in an adolescent girl.
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چکیده
To cite: Kumar S, Rajagopal KV, Karegowda LH, et al. BMJ Case Rep Published online: [please include Day Month Year] doi:10.1136/bcr-2015209638 DESCRIPTION A 14-year-old girl presented to emergency triage with acute retention of urine. There was history of cyclic pelvic pain for the past 6 months, for which she had been prescribed non-steroidal antiinflammatory drugs by a private practitioner. There was no history of ureteric colic or burning during micturition. Gynaecological history indicated menarche at 12 years followed by regular menses. There was no history of abnormal vaginal bleeding. Ultrasound of the abdomen revealed findings suggestive of bicornuate uterus with haematocolpos. Subsequently, MRI was requisitioned, revealing two widely divergent, symmetrical uterine corpii, partially fused at the cervix without any communication between their endometrial cavities (figure 1A). There was a thick hypointense left hemivaginal septum with a large ipsilateral haematocolpos appearing hyperintense on T1-weighted and hypointense on T2-weighted images, findings consistent with intracellular methaemoglobin stage of bleed. A similar intensity dilated tortuous
منابع مشابه
Herlyn Werner Wunderlich Syndrome with Hematocolpos: An Unusual Case Report of Full Diagnostic Approach and Treatment
Herlyn-Werner-Wunderlich (HWW) syndrome is an uncommon combined müllerian duct anomalies (MDAs) and mesonephric duct malformation of female urogenital tract characterized by uterus didelphys and obstructed hemi-vagina and ipsilateral renal agenesis (OHVIRA) syndrome. We present a rare and unusual case of this syndrome in a 19 year-old female who suffered from hypomenorrhoea and abdominal pain. ...
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Herlyn-Werner-Wunderlich (HWW) syndrome is a very rare congenital anomaly of the urogenital tract resulting from maldevelopment of both Mullerian and Wolffian ducts. It is characterized by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. It generally presents at puberty shortly following menarche with the symptom of acute pelvic pain. Management of these case...
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Herlyn-Werner-Wunderlich (HWW) syndrome is a rare developmental anomaly that includes uterus didelphys with obstructed hemivagina and ipsilateral renal agenesis. A 13-year-old girl presented with chronic abdominal pain. Magnetic resonance imaging revealed uterus didelphys, hematometrocolpos and renal agenesis on the right side with imperforate hymen. Subsequently the patient was found to have M...
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Uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis is a rare congenital anomaly of the Müllerian duct system referred to as Herlyn-Werner-Wunderlich syndrome. Because of its rare occurrence, a high level of suspicion is often required for diagnosis. Clinically, these patients usually present after menarche with pelvic pain, dysmenorrhea, and a palpable pelvic mass. We p...
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ورودعنوان ژورنال:
- BMJ case reports
دوره 2015 شماره
صفحات -
تاریخ انتشار 2015